Ultrasound of the carotid and subclavian arteries can aid in early diagnosis of the disease. Takayasu arteritis, with variants called pulseless disease, branchial arteritis, and giantcell arteritis of the aorta, involves principally the thoracic aorta chest portion and the adjacent segments of its large branches. Other articles where takayasus disease is discussed. Symptoms, including diminished or absent pulses in the arms. Seventeen surgical biopsy specimens of the axillary or subclavian artery were obtained from patients who had inflammatory, nonatherosclerotic arterial lesions and were studied retrospectively. The mean age at presentation of our cases was 11 years range 815. To evaluate prospectively the clinical features, angiographic findings, and response to treatment of patients with takayasu arteritis. It is a relatively rare disease, which presents with a wide spectrum of clinical features. Takayasuarteritis arteritis, takayasu pulseless disease takayasusyndrom. The disease results from an attack by the bodys own immune system, causing inflammation in the walls of arteries.
Examination showed a difference of 40 mm hg in systolic blood pressure between the 2 arms. Back pain is, however, rarely described to be a presenting symptom of ta. A 19yearold woman presented with a 4month history of fatigue, weight loss, and thrombocytosis. Cest une aortoarterite non specifique touchant laorte, les arteres qui en naissent et les arteres pulmonaires. Tak affects the aorta and its main branches, which carry blood from the heart to the rest of the body. We report a case of a 28yearold female with no known comorbidity, who presented with back pain along with. Intensive care unit icu admission is indicated for patients with critical deterioration. Takayasus arteritis tak is a form of vasculitisa family of rare disorders characterized by inflammation of the blood vessels, which can restrict blood flow and damage vital organs and tissues. Initial roentgenologic clinical, and histologic findings were evaluated and compared with final diagnosis. Examination showed a difference of 40 mm hg in systolic blood pressure between the 2 arms, together. Takayasus arteritis also known as, aortic arch syndrome, nonspecific aortoarteritis, and pulseless disease. Dans une etude nordamericaine, lincidence est estimee a 2,6 casmillionsan1. Takayasu arteritis in children europe pmc article europe pmc.
To date, familial cases of ta have been considered rare. Arterite a cellules geantes arterite temporale arterite granulomateus. Takayasus arteritis american college of rheumatology. Takayasu arteritis ta is a rare chronic inflammatory disease of the aorta and its major branches. Takayasu s arteritis also known as, aortic arch syndrome, nonspecific aortoarteritis, and pulseless disease. Aortic valve replacement for acute takayasus disease. Histological examination suggested takayasu s disease in 11 patients whereas the roentgenologic. Hong cy, yung ys, choi jy, sul jh, lee ks, cha sh, et al. Takayasus teritis with surgically corrected severe aortic valvular reg gitation. Mr images of 77 patients with ta 74 women, three men were obtained with a 1. Histological examination suggested takayasus disease in 11 patients whereas the roentgenologic.
Takayasu arteritis ta is a large vessel vasculitis that usually affects young female patients during the second and third decades of life, but has been reported in children as young as 24 months of age. Takayasu arteritis ta is a chronic inflammatory largevessel vasculitis of the aorta and its major branches. Takayasu arteritis in children pediatric rheumatology. Inpatient care is limited to managing acute manifestations of the disease, which usually result in complications from organ failure, stroke, pregnancy, seizures, and intracranial hemorrhage. Takayasus arteritis, also called tak, is a rare form of vasculitis disease involving inflammation in the walls of the largest arteries in the body. Mk, pasquier g, herreman f, bonnin a, fouchard j, houille f. Takayasu arteritis is a rare, systemic, inflammatory largevessel vasculitis of unknown etiology that most commonly affects women of childbearing age. The macaroni sign of takayasus arteritis the journal of. The arterial revascularization should also be considered if necessary and regular monitoring is mandatory. Sep 28, 2008 takayasu arteritis ta is a large vessel vasculitis that usually affects young female patients during the second and third decades of life, but has been reported in children as young as 24 months of age. Takayasu disease definition of takayasu disease by medical. Takayasu arteritis in korean children clinical report of seventy cases.
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